Papillon-Lefevre Syndrome [Papillon-Lefevre Sendromu]
Küçük Resim Yok
Tarih
2007
Yazarlar
Dergi Başlığı
Dergi ISSN
Cilt Başlığı
Yayıncı
Erişim Hakkı
info:eu-repo/semantics/closedAccess
Özet
Papillon-Lefevre Syndrome is an extremely rare genetic disorder that typically effects infants of approximately one to 5 years of age. Papillon-Lefevre Syndrome is characterized by the development of palmar-plantar hyperkeratosis and early loss of the primary (deciduous) and permanent teeth due to rapidly progressive periodontopathy. The primary (deciduous) teeth frequently become loose and fall out by about five years of age. In the general population, the disorder occurs in approximately one to 4 individuals per 1.000.000. Here we present a Papillon-Lefevre Syndrome case, which is rarely seen, with a review of the literature.
Açıklama
Anahtar Kelimeler
Keratoderma palmoplantar, Papillon-Lefevre disease, Periodontitis juvenile
Kaynak
Erciyes Tip Dergisi
WoS Q Değeri
Scopus Q Değeri
N/A
Cilt
29
Sayı
6
