Amniotic band syndrome associated with cranial defects and ectopia cordis: Two case report
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Dosyalar
Tarih
2005
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Cilt Başlığı
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Erişim Hakkı
info:eu-repo/semantics/openAccess
Özet
Amniyotik band sendromu; amputasyonlar, disunion, konstriksiyona yol açan bandlar ve karın duvarı defektleri ile seyreden kompleks bir bozukluktur. Amniyotik band sendromu, kompleks fizyopatolojik mekanizmaya sahiptir. Bu yazıda otopside amniyotik band sendromu tanısını alan iki olguyu tanımladık. ilk olguda prenatal ultrasonografide kraniyal deformiteler, ectopia kordis, fasiyal yarıklar ve gastroflizis saptanmışken, ikinci olguda sadece ultrasonografi ile frontal ensefalosel tespit edildi. Her iki olguda da amniyotik bandlar postmortem incelemede saptandı. Ventral defektlerin, fasiyal yarıkların ve kraniyal deformitelerin saptandığı olgularda amniyotik bandların araştırılması gereklidir.
Amniotic band syndrome is a group of disorders characterized by amputations, disunion, constricting bands and body wall defects. Amniotic band syndrome or amnion disruption sequence had complex pathophysiological mechanism. We described the diagnosis of two cases of amniotic band syndrome by postmortem examination. In the first case, cranial deformation, ectopia cordis, facial cleft and gastroschisis were detected by ultrasound. In the second case, ultrasonography has revealed a frontal encephalocele. In both cases amniotic bands were detected at postmortem examination. This report indicates the importance of detailed search for amniotic bands when body wall defects, facial clefts and cranial deformations are diagnosed.
Amniotic band syndrome is a group of disorders characterized by amputations, disunion, constricting bands and body wall defects. Amniotic band syndrome or amnion disruption sequence had complex pathophysiological mechanism. We described the diagnosis of two cases of amniotic band syndrome by postmortem examination. In the first case, cranial deformation, ectopia cordis, facial cleft and gastroschisis were detected by ultrasound. In the second case, ultrasonography has revealed a frontal encephalocele. In both cases amniotic bands were detected at postmortem examination. This report indicates the importance of detailed search for amniotic bands when body wall defects, facial clefts and cranial deformations are diagnosed.
Açıklama
Anahtar Kelimeler
Kadın Hastalıkları ve Doğum
Kaynak
Journal of the Turkish-German Gynecological Association
WoS Q Değeri
Scopus Q Değeri
Cilt
6
Sayı
4
