Tuberoskleroz Kompleksli Hastada Hemorajik Giant Renal Anjiomyolipom’a Nefron Koruyucu Cerrahi Yaklaşım: Olgu Sunumu
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Tarih
2016 Aralık
Dergi Başlığı
Dergi ISSN
Cilt Başlığı
Yayıncı
Selçuk Üniversitesi
Erişim Hakkı
info:eu-repo/semantics/openAccess
Özet
Tuberoskleroz, tüm organları tutabilen ancak en sık deri, beyin, kalp, göz ve böbreği tutan benign hamartomatöz lezyonlar ile karakterize otozomal dominant bir hastalıktır. Renal anjiomyolipom (AML) matür yağ hücreleri, düz kas dokusu ve kalın duvarlı kan damarlarını değişen oranlarda içeren benign bir tümördür. Tuberoskleroz kompleksinin (TS) en yaygın ürolojik tutulumu renal anjiomyolipomlardır. Anjiomyolipomlar asemptomatik olabilmekle beraber, palpabl kitle, ağrı, hematüri şikayeti ile tanı alabilir, masif kanamaya neden olarak morbidite ve mortaliteye sebep olabilirler. Biz de palpable kitle ile tanı konulan, masif kanamaya neden olan ve cerrahi tedavi yapılan dev renal anjiomyolipom olgumuzu paylaşmak ve bulgular eşliğinde güncel literatürü değerlendirmek istedik.
Tuberous sclerosis is an autosomal dominant disease characterized with benign hamartomatosis lesions which may involve all organs but most commonly involve skin, brain, heart, eye and kidney. Renal angiomyolipoma (AML) is a benign tumor including mature fat cells, flat muscle tissue and thick walled blood vessels in different ratios. Angiomyolipomas are the most common urological involvement of tuberous sclerosis complex (TS). Although angiomyolipomas may be asymptomatic, they can be diagnosed with palpable mass, pain and hematuria complaint and may cause morbidity and mortality by massive bleeding. We wanted to share our giant renal angiomyolipoma case which was diagnosed with a palpable mass and caused a massive bleeding and was treated surgically and review the current literature with the findings.
Tuberous sclerosis is an autosomal dominant disease characterized with benign hamartomatosis lesions which may involve all organs but most commonly involve skin, brain, heart, eye and kidney. Renal angiomyolipoma (AML) is a benign tumor including mature fat cells, flat muscle tissue and thick walled blood vessels in different ratios. Angiomyolipomas are the most common urological involvement of tuberous sclerosis complex (TS). Although angiomyolipomas may be asymptomatic, they can be diagnosed with palpable mass, pain and hematuria complaint and may cause morbidity and mortality by massive bleeding. We wanted to share our giant renal angiomyolipoma case which was diagnosed with a palpable mass and caused a massive bleeding and was treated surgically and review the current literature with the findings.
Açıklama
Anahtar Kelimeler
Renal Anjiomyolipom, Tuberoskleroz, Nefron Koruyucu Cerrahi, Renal angiomyolipoma, Tuberous Sclerosis, Nephron sparing surgery
Kaynak
Selçuk Genel Tıp Dergisi
WoS Q Değeri
Scopus Q Değeri
Cilt
26
Sayı
4
Künye
Sönmez, M. G., Haliloğlu, A. H., Tangal, S., Göğer, Y. E., Demirelli, E., (2016). Tuberoskleroz Kompleksli Hastada Hemorajik Giant Renal Anjiomyolipom’a Nefron Koruyucu Cerrahi Yaklaşım: Olgu Sunumu. Selçuk Genel Tıp Dergisi, 26(4), 134-138.
