En coup de sabre accompanied by pachydermoperiostosis: a case report
Küçük Resim Yok
Tarih
2007
Yazarlar
Dergi Başlığı
Dergi ISSN
Cilt Başlığı
Yayıncı
CLINICAL & EXPER RHEUMATOLOGY
Erişim Hakkı
info:eu-repo/semantics/closedAccess
Özet
Scleroderma en coup de sabre, a variant of localized scleroderma is a disorder characterized by fibrosis of connective tissue. We report a 21-year-old female with scleroderma en coup de sabre accompanied by pachydermoperiostosis. She was born to consanguineous parents and her older siser also had pachydermoperiostosis characterized by clubbing of the digits, enlargement of distal parts of the extremities. The two disorders were diagnosed by clinical examination, histological and x-ray findings. In contrast to scleroderma, pachydermoperiostosis is a hypertrophic process characterized by periosteal proliferation of the tubuler bones and hypertrophic skin changes. We discuss this interesting coexistence and review the literature.
Açıklama
Anahtar Kelimeler
en coup de sabre, pachydermoperiostosis, human fibrosis
Kaynak
CLINICAL AND EXPERIMENTAL RHEUMATOLOGY
WoS Q Değeri
Q2
Scopus Q Değeri
Q2
Cilt
25
Sayı
2
