A case of congenital agenesis of the right pulmonary artery presenting with hemoptysis and mimicking pulmonary hemosiderosis

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dc.contributor.authorSimsek, Pelin Ozlem
dc.contributor.authorOzcelik, Ugur
dc.contributor.authorCeliker, Alpay
dc.contributor.authorYalcin, Ebru
dc.contributor.authorCobanoglu, Nazan
dc.contributor.authorPekcan, Sevgi
dc.contributor.authorAlehan, Dursun
dc.date.accessioned2020-03-26T17:37:42Z
dc.date.available2020-03-26T17:37:42Z
dc.date.issued2009
dc.departmentSelçuk Üniversitesien_US
dc.description.abstractCongenital unilateral absence of a pulmonary artery is a rare anomaly most frequently accompanied by other cardiovascular anomalies. We report a 10-year-old girl presenting with fatigue and recurrent hemoptysis who was initially misdiagnosed with idiopathic pulmonary hemosiderosis. Her symptoms did not resolve despite treatment so she was referred to our center for further evaluation. We carried out an angiography which revealed the absence of the right pulmonary artery and multiple collaterals originating from the right subclavian and right internal mammary arteries supplying the right lung. During the follow-up the patient developed a severe episode of pulmonary infection and pulmonary hypertension which responded well to medical treatment. Physicians should be aware of the congenital absence of the right pulmonary artery especially in patients presenting with recurrent respiratory symptoms. Although this condition is generally considered to have a good prognosis, close observation is mandatory in order to prevent further complications and comorbidities.en_US
dc.identifier.doi10.1007/s00431-008-0726-xen_US
dc.identifier.endpage220en_US
dc.identifier.issn0340-6199en_US
dc.identifier.issn1432-1076en_US
dc.identifier.issue2en_US
dc.identifier.pmid18478262en_US
dc.identifier.scopusqualityQ1en_US
dc.identifier.startpage217en_US
dc.identifier.urihttps://dx.doi.org/10.1007/s00431-008-0726-x
dc.identifier.urihttps://hdl.handle.net/20.500.12395/23195
dc.identifier.volume168en_US
dc.identifier.wosWOS:000261951800015en_US
dc.identifier.wosqualityQ2en_US
dc.indekslendigikaynakWeb of Scienceen_US
dc.indekslendigikaynakScopusen_US
dc.indekslendigikaynakPubMeden_US
dc.language.isoenen_US
dc.publisherSPRINGERen_US
dc.relation.ispartofEUROPEAN JOURNAL OF PEDIATRICSen_US
dc.relation.publicationcategoryMakale - Uluslararası Hakemli Dergi - Kurum Öğretim Elemanıen_US
dc.rightsinfo:eu-repo/semantics/closedAccessen_US
dc.selcuk20240510_oaigen_US
dc.subjectCongenital right pulmonary artery agenesisen_US
dc.subjectCollateralsen_US
dc.subjectPulmonary hypertensionen_US
dc.titleA case of congenital agenesis of the right pulmonary artery presenting with hemoptysis and mimicking pulmonary hemosiderosisen_US
dc.typeArticleen_US

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