Parry-Romberg Syndrome Facial Atrophy and Its Relationship With Other Regions of the Body

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dc.contributor.authorDuymaz, Ahmet
dc.contributor.authorKarabekmez, Furkan Erol
dc.contributor.authorKeskin, Mustafa
dc.contributor.authorTosun, Zekeriya
dc.date.accessioned2020-03-26T17:39:33Z
dc.date.available2020-03-26T17:39:33Z
dc.date.issued2009
dc.departmentSelçuk Üniversitesien_US
dc.description.abstractParry-Romberg syndrome (PRS) is an uncommon disorder and characterized by a slowly, an acquired progressive atrophy involving skin, loft tissue, cartilage, and bony structures. Accompanying atrophies of the other parts of the body are rarely reported. The aim of this study is to report a case that had contralateral lower extremity atrophy with PRS, and to review he related etiologic features, physiopathology, and mechanism. The patient who admitted for his facial atrophy also had atrophy of his contralateral extremity. This extremity was also short in length when compared with other extremity. To obtain detailed information regarding the severity of involvement routine laboratory investigations including antinuclear antibody (ANA), magnetic resonance imagine (MRI) of the craniofacial region and lower extremities, MR angiography of the lower extremities and brain, 3-dimension computed tomography (CT) scan of the craniofacial region were performed. Normal or negative laboratory findings included results of blood count, renal and hepatic function biochemical test's, rheumatoid factor, C-reactive protein, anti-dsDNA antibody except ANA that were positive, His lower extremity and brain MR angiography were normal. in the 3-dimensional cranial CT, there was no abnormality or defect in the bony structures. His brain MRI showed no pathologic changes, and his facial MRI demonstrated noteworthy atrophy to the sternocleidomastoid, masseter, pterygoid muscles, and subcutaneus soft tissues on the right side of the face. Additionally, MR investigation of his lower extremities revealed decreased volume in muscles and bony structures of the effected extremity compared, with the other extremity, but pathologic evidence of fatty degeneration associated with muscle atrophy was not demonstrated. The patient had isolated contralateral lower extremity involvement combined with hemifacial atrophy (without affecting any other part of the body). Although more accepted theory is the sympathic nervous system dysfunction, autoimmunity may play a roll in the etiology of our case as ANA abnormality was found in multiple tests.en_US
dc.identifier.doi10.1097/SAP.0b013e31818bed6den_US
dc.identifier.endpage461en_US
dc.identifier.issn0148-7043en_US
dc.identifier.issn1536-3708en_US
dc.identifier.issue4en_US
dc.identifier.pmid19745718en_US
dc.identifier.scopusqualityQ2en_US
dc.identifier.startpage457en_US
dc.identifier.urihttps://dx.doi.org/10.1097/SAP.0b013e31818bed6d
dc.identifier.urihttps://hdl.handle.net/20.500.12395/23742
dc.identifier.volume63en_US
dc.identifier.wosWOS:000270209000024en_US
dc.identifier.wosqualityQ3en_US
dc.indekslendigikaynakWeb of Scienceen_US
dc.indekslendigikaynakScopusen_US
dc.indekslendigikaynakPubMeden_US
dc.language.isoenen_US
dc.publisherLIPPINCOTT WILLIAMS & WILKINSen_US
dc.relation.ispartofANNALS OF PLASTIC SURGERYen_US
dc.relation.publicationcategoryDiğeren_US
dc.rightsinfo:eu-repo/semantics/closedAccessen_US
dc.selcuk20240510_oaigen_US
dc.subjectParry-Romberg syndromeen_US
dc.subjectlower extremity involvementen_US
dc.titleParry-Romberg Syndrome Facial Atrophy and Its Relationship With Other Regions of the Bodyen_US
dc.typeReviewen_US

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