Neuro-Behçet disease presented with pachymeningitis in a child [Enfermedad de neuro-Behçet con paquimeningitis en una niña]
Yükleniyor...
Dosyalar
Tarih
2019
Dergi Başlığı
Dergi ISSN
Cilt Başlığı
Yayıncı
Sociedad Argentina de Pediatria
Erişim Hakkı
info:eu-repo/semantics/openAccess
Özet
Behçet’s disease (BD) is a rare systemic vasculitis disorder of unknown etiology characterized by recurrent oral and genital apthae and uveitis. It involves the central or peripheral nervous system; occurs rarely during childhood. Isolated acute aseptic meningitis is extremely uncommon. We report here a case of Neuro-Behçet disease (NBD) diagnosed in a 14-year-old girl. The patient presented acute headache, diplopia, papilla edema, and meningeal irritation. She had a history of recurrent oral ulcers. Brain magnetic resonance imaging revealed pachymeningitis. Pleocytosis and pressure increase were the cerebrospinal fluid findings. Although medical therapy, her complaints were not resolved. Uveitis was not detected, pathergy test was negative. HLA-B51 allele was positive. The findings were considered to unusual NBD. The patient improved dramatically after steroid therapy. BD should be considered in differential diagnosis of meningitis unless an infectious agent is demonstrated. To our knowledge, a case of pachymeningitis with NBD, was not described in children.
Açıklama
Anahtar Kelimeler
Behçet’s syndrome, aseptic meningitis, children
Kaynak
Archivos Argentinos de Pediatria
WoS Q Değeri
Scopus Q Değeri
Q3
Cilt
117
Sayı
6
Künye
Alkan, G., Kartal, A., Emiroğlu, M., Paksoy, Y. (2019). Neuro-Behçet Disease Presented With Pachymeningitis in a Child [Enfermedad de Neuro-Behçet Con Paquimeningitis en Una Niña]. Archivos Argentinos de Pediatria, 117,(6), E644-E647.
