Neuro-Behçet disease presented with pachymeningitis in a child [Enfermedad de neuro-Behçet con paquimeningitis en una niña]

dc.contributor.authorAlkan, Gülsüm
dc.contributor.authorKartal, Ayşe
dc.contributor.authorEmiroğlu, Melike
dc.contributor.authorPaksoy, Yahya
dc.date.accessioned2020-03-26T20:19:47Z
dc.date.available2020-03-26T20:19:47Z
dc.date.issued2019
dc.departmentSelçuk Üniversitesi, Tıp Fakültesi, Dahili Tıp Bilimleri Bölümüen_US
dc.description.abstractBehçet’s disease (BD) is a rare systemic vasculitis disorder of unknown etiology characterized by recurrent oral and genital apthae and uveitis. It involves the central or peripheral nervous system; occurs rarely during childhood. Isolated acute aseptic meningitis is extremely uncommon. We report here a case of Neuro-Behçet disease (NBD) diagnosed in a 14-year-old girl. The patient presented acute headache, diplopia, papilla edema, and meningeal irritation. She had a history of recurrent oral ulcers. Brain magnetic resonance imaging revealed pachymeningitis. Pleocytosis and pressure increase were the cerebrospinal fluid findings. Although medical therapy, her complaints were not resolved. Uveitis was not detected, pathergy test was negative. HLA-B51 allele was positive. The findings were considered to unusual NBD. The patient improved dramatically after steroid therapy. BD should be considered in differential diagnosis of meningitis unless an infectious agent is demonstrated. To our knowledge, a case of pachymeningitis with NBD, was not described in children.en_US
dc.identifier.citationAlkan, G., Kartal, A., Emiroğlu, M., Paksoy, Y. (2019). Neuro-Behçet Disease Presented With Pachymeningitis in a Child [Enfermedad de Neuro-Behçet Con Paquimeningitis en Una Niña]. Archivos Argentinos de Pediatria, 117,(6), E644-E647.
dc.identifier.doi10.5546/AAP.2019.E644en_US
dc.identifier.endpageE647en_US
dc.identifier.issn0325-0075en_US
dc.identifier.issue6en_US
dc.identifier.pmid31758902en_US
dc.identifier.scopusqualityQ3en_US
dc.identifier.startpageE644en_US
dc.identifier.urihttps://dx.doi.org/10.5546/AAP.2019.E644
dc.identifier.urihttps://hdl.handle.net/20.500.12395/38399
dc.identifier.volume117en_US
dc.indekslendigikaynakScopusen_US
dc.indekslendigikaynakPubMeden_US
dc.institutionauthorKartal, Ayşe
dc.institutionauthorEmiroğlu, Melike
dc.institutionauthorPaksoy, Yahya
dc.language.isoesen_US
dc.publisherSociedad Argentina de Pediatriaen_US
dc.relation.ispartofArchivos Argentinos de Pediatriaen_US
dc.relation.publicationcategoryMakale - Uluslararası Hakemli Dergi - Kurum Öğretim Elemanıen_US
dc.rightsinfo:eu-repo/semantics/openAccessen_US
dc.selcuk20240510_oaigen_US
dc.subjectBehçet’s syndrome
dc.subjectaseptic meningitis
dc.subjectchildren
dc.titleNeuro-Behçet disease presented with pachymeningitis in a child [Enfermedad de neuro-Behçet con paquimeningitis en una niña]en_US
dc.typeArticleen_US

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